Glanzmann thrombasthenia – presenting as prolonged severe bleeding following minor trauma

RN Morawakkorala, AMRD Senarathana, ACD de Alwis, V Rathnamalala

Abstract


Glanzmann thrombasthenia (GT) is an inherited
haemorrhagic disorder characterized by a severe
reduction in, or absence of, platelet aggregation in
response to multiple agonists due to qualitative or
quantitative abnormalities of platelet glycoprotein
(GP) 11b and/or 111a. Glanzmann, a Swiss
paediatrician, described a group of patients with
haemorrhagic symptoms especially of nasopharynx in
1918.

Key words: Glanzmann thrombasthenia

DOI = 10.4038/sljch.v35i1.8

Sri Lanka Journal of Child Health, 2006; 35: 36-7


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Sri Lanka Journal of Child Health ISSN:1391-5452

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SLJOL is supported by INASP